JUVENILE XANTHOGRANULOMA: A RARITY

CECÍLIA SALAZAR ULACIA, ALEXANDRE RODRIGUES ALVES, FREDERICO VIEIRA MOTA, JESSICA DOS ANJOS HUANG, POLLYANA LOPES DE ARAUJO, ADRIANA CARTAFINA PEREZ -BÓSCOLLO

ABSTRACT

Juvenile xanthogranuloma is a rare and benign pathology, belonging to the vast group of non-Langerhans histiocytosis. It typically appears in pediatric age and may have a neonatal presentation. Involvement is predominantly cutaneous in the form of yellow and/or erythematous papules or nodules, asymptomatic, solitary or multiple. Extracutaneous involvement is more common in children under two years of age and with multiple injuries, with the eye being the most affected site. We highlight this clinical case due to its unusual presentation on the scalp, similar to a trichilemmal cyst.

Keywords: Juvenile xanthogranuloma; Non-Langerhans